Multiple glomus tumors and segmental neurofibromatosis: there are no coincidences.
نویسندگان
چکیده
Segmental neurofibromatosis is a rare subtype of neurofibromatosis type 1 (NF1). Glomus tumors are uncommon benign tumors. The authors report the association between these two rare conditions, not yet reported.
منابع مشابه
Glomus Tumors and Neurofibromatosis: A Newly Recognized Association
BACKGROUND Glomus tumors are painful benign tumors arising from the neuromyoarterial elements of the glomus body, typically in a subungual location. Historically, glomus tumors have been considered isolated or sporadic, not typically associated with other disease processes. Over the last few years, however, multiple case reports, a molecular genetics study, and an epidemiologic study have confi...
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Two cases of multiple concomitant CNS tumors of different histologic types are presented. One was a case of neurofibromatosis type 2 (NF2) with 6 CNS tumors, and the other a case of 4 CNS tumors without any evidence of NF. To our knowledge, there is no report of concomitant occurrence of 6 CNS tumors in the medical literature. Neuroradiological and operative findings are illustrated and discu...
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BACKGROUND Glomus tumors have recently been reported in individuals with the neurofibromatosis type 1 (NF1) cancer disposition syndrome. We compare the clinical and molecular features of these painful hamartomas in a series of sporadic and NF1-associated cases. OBJECTIVE We sought to evaluate the association of NF1 with glomus tumors and to compare NF1-associated glomus tumors with sporadic g...
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عنوان ژورنال:
- Dermatology online journal
دوره 17 3 شماره
صفحات -
تاریخ انتشار 2011